pulmonary hypertension

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Introduction

Chronic disorder with mean pulmonary artery pressure of > 20-25 mm Hg at rest or > 30 mm Hg with exercise & a pulmonary capillary wedge pressure < 15 mm Hg measured during right heart catheterization.*

* see Differential diagnosis: below for causes of acute elevation in pulmonary artery pressure.

Etiology

* left heart disease & hypoxemia due to chronic lung disease most common causes[3]

* see causes of pulmonary hypertension for more detail

Pathology

* increased mean pulmonary artery pressure with elevated pulmonary artery capillary wedge pressure indicates pulmonary venous hypertension

Genetics

Clinical manifestations

(also see primary pulmonary hypertension)

Laboratory

Diagnostic procedures

Radiology

Complications

* mean pulmonary artery pressure of 19-24 mm Hg

Differential diagnosis

Management

More general terms

More specific terms

Additional terms

References

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    Medical Knowledge Self Assessment Program (MKSAP) 19 Board Basics. An Enhancement to MKSAP19. American College of Physicians, Philadelphia 2022
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