primary pulmonary hypertension (PPH)

From Aaushi
Jump to navigation Jump to search

Introduction

Primary pulmonary hypertension (PPH) is an uncommon disease of unknown etiology. It occurs most often in young to middle-aged women & usually results in death within several years of diagnosis.

Etiology

Epidemiology

  • uncommon
  • may occur from infancy throughout life
  • primarily in young to middle-aged women
    • mean age at onset of 36 years

Pathology

Clinical manifestations

Diagnostic criteria

by exclusion

Laboratory

Diagnostic procedures

Radiology

Management

More general terms

More specific terms

References

  1. 1.0 1.1 Manual of Medical Therapeutics, 28th ed, Ewald & McKenzie (eds), Little, Brown & Co, Boston, 1995, pg 256
  2. 2.0 2.1 Mayo Internal Medicine Board Review, 1998-99, Prakash UBS (ed) Lippincott-Raven, Philadelphia, 1998, pg 779
  3. 3.0 3.1 3.2 Medical Knowledge Self Assessment Program (MKSAP) 11, 14, American College of Physicians, Philadelphia 1998, 2006