aortic subvalvular stenosis

Classification

• two major types:
• discrete or membranous
• fibromuscular (fixed or dynamic) (hypertrophic cardiomyopathy)

Etiology

congenital malformation

Pathology

• commonly associated with aortic regurgitation
• high pressure gradient from left ventricle to aorta

Clinical manifestations

• prominent left ventricle
• reduced pulse pressure
• no ejection click
• arterial thrill when stenosis is severe
• hypertrophic obstructive cardiomyopathy
  • ejection murmur at left sternal border
  • prominent pulses with a bifid quality

Radiology

• 2-D & doppler echocardiography
• left heart cardiac catheterization

More general terms

• heart disease (cardiac disease)

Additional terms

• aortic valvular stenosis (AS)
• hypertrophic cardiomyopathy (HCM), including idiopathic hypertrophic subaortic stenosis (IHSS)