paraneoplastic brainstem encephalitis; paraneoplastic rhombencephalitis
Jump to navigation
Jump to search
Etiology
- mediator: unknown
- KLHL11 autoimmunity[2][3]
- associated neoplasms:
Pathology
Clinical manifestations
- evolution over weeks to months
- nystagmus
- diplopia
- vertigo
- ataxia
- dysarthria
- dysphagia
- memory loss with progession to dementia
More general terms
References
- ↑ Harrison's Principles of Internal Medicine, 14th ed. Fauci et al (eds), McGraw-Hill Inc. NY, 1998, pg 624
- ↑ 2.0 2.1 2.2 Devine MF, Gay PC, Dubey D Ondine's Curse and Trismus in Association With Kelch-like Protein-11 Autoimmunity. JAMA Neurol. Published online May 28, 2021 PMID: https://www.ncbi.nlm.nih.gov/pubmed/34047764 https://jamanetwork.com/journals/jamaneurology/fullarticle/2780425
- ↑ 3.0 3.1 Dubey D, Wilson MR, Clarkson B et al Expanded Clinical Phenotype, Oncological Associations, and Immunopathologic Insights of Paraneoplastic Kelch-like Protein-11 Encephalitis. JAMA Neurol. 2020 Nov 1;77(11):1420-1429 PMID: https://www.ncbi.nlm.nih.gov/pubmed/32744608
- ↑ 4.0 4.1 Mandel-Brehm C, Dubey D, Kryzer TJ et al Kelch-like Protein 11 Antibodies in Seminoma-Associated Paraneoplastic Encephalitis. N Engl J Med. 2019 Jul 4;381(1):47-54 PMID: https://www.ncbi.nlm.nih.gov/pubmed/31269365 Free PMC article
- ↑ Lawn ND, Westmoreland BF, Kiely MJ, Lennon VA, Vernino S. Clinical, magnetic resonance imaging, and electroencephalographic findings in paraneoplastic limbic encephalitis Mayo Clin Proc. 2003 Nov;78(11):1363-8. PMID: https://www.ncbi.nlm.nih.gov/pubmed/14601695