choroid plexus papilloma

Epidemiology

• primary choroid plexus tumors are rare & usually occur in early childhood

Pathology

• slow-growing benign tumor of the choroid plexus
• often invades the leptomeninges
• in children it is usually in a lateral ventricle but in adults it is more often in the 4th ventricle
• hydrocephalus is common, either from obstruction or from tumor secretion of cerebrospinal fluid

Genetics

• defects in TP53

Complications

• if it undergoes malignant transformation it is called a choroid plexus carcinoma

More general terms

• choroid plexus neoplasm

Patient information

choroid plexus papilloma patient information

Database

• OMIM: https://mirror.omim.org/entry/260500