Diagnostic Criteria for Hypermobile Ehlers-Danlos Syndrome (hEDS, Beighton Score)

^[1]

Indications

criterion 1
- can you or could you place your hands flat on the floor without bending your knees?
- can you or could you bend your thumb to touch your forearm?
- can you or could you do the splits?
- has your shoulder or kneecap dislocated on > 1 occasion?
- do you consider yourself 'double-jointed'?
criterion 2
- feature A (5/12 must be present)
  - unusually soft or velvety skin
  - mild skin hyperextensibility
  - unexplained striae distensae or rubae*
  - bilateral piezogenic papules of the heel
  - recurrent or multiple abdominal hernia(s)
  - atrophic scarring involving at least 2 sites*
  - pelvic floor, rectal, and/or uterine prolapse*
  - dental crowding and high or narrow palate
  - arachnodactyly*
  - arm span-to-height ratio >= 1.05
  - mitral valve prolapse >= mild
  - aortic root dilatation*
- feature B positive family history (>= 1 1st degree relative)
- feature C recurrent joint dislocations in absence of trauma
criterion 3
- absence of unusual skin fragility
- exclusion of genetic disease, autoimmune disease or connective tissue disease
- exclusion of alternative diagnoses

* see ref^[1] for more complete description