3-ketoacyl CoA thiolase (beta-ketothiolase, ACAA)

Function

• lipid metabolism fatty acid metabolism

acyl-CoA + acetyl-CoA <--> CoA + 3-oxoacyl-CoA

Structure

• homotetramer
• belongs to the thiolase family

More general terms

• thiolase

More specific terms

• 3-ketoacyl CoA thiolase mitochondrial (beta-ketothiolase, thiolase-1, ACAA2)
• acetyl-Coenzyme A acyltransferase 1 (peroxisomal 3-ketoacyl CoA thiolase, peroxisomal 3-oxoacyl-Coenzyme A thiolase, beta-ketothiolase, thiolase-3, ACAA1, ACAA, PTHIO)

Additional terms

• alpha-methylacetoaceticaciduria; 3-ketoacyl CoA thiolase deficiency