Dowling-Degos-Kitamura disease; Dowling-Degos disease; reticulate acropigmentation of Kitamura
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Genetics
- autosomal dominant
- associated with defects in KRT5
Clinical manifestations
- postpubertal reticulate hyperpigmentation, progressive & disfiguring
- small hyperkeratotic dark brown papules affect mainly the flexures & great skin folds
- generally, no abnormalities of the hair or nails