mitochondrial trifunctional enzyme complex (trifunctional protein complex, TFP complex, trifunctional enzyme)

Structure

• consists of:
  • trifunctional enzyme alpha subunit (HADHA)
  • trifunctional enzyme beta subunit (HADHB)

Pathology

• deficiency of all 3 enzyme activities associated with trifunctional protein deficiency

More general terms

• molecular complex
• mitochondrial protein

Additional terms

• trifunctional protein deficiency (TFP deficiency)