succinyl-CoA sunthetase alpha subunit (succinyl-CoA ligase [GDP-forming] alpha-chain, SCS-alpha, SUCLG1)

Function

• subunit of Succinyl-CoA sunthetase
• carbohydrate metabolism; tricarboxylic acid cycle

Structure

• belongs to the succinate/malate CoA ligase alpha subunit family

Compartment

mitochondria

Pathology

• defects in SUCLG1 are a cause of fatal infantile lactic acidosis

More general terms

• mitochondrial protein
• protein subunit

Component of

• succinyl CoA synthetase (GDP-formining)

Database

• Kegg: http://www.genome.jp/dbget-bin/www_bget?hsa:8802
• OMIM: https://mirror.omim.org/entry/245400
• UniProt: http://www.uniprot.org/uniprot/P53597.html