chronic pulmonary fibrosis

Etiology

connective tissue disorder

Clinical manifestations

• indistinquishable from idiopathic pulmonary fibrosis
• progressive exertional dyspnea presenting months to years after diagnosis of underlying connective tissue disorder

Differential diagnosis

• esophageal dysfunction with chronic aspiration
  • scleroderma
  • mixed connective tissue disease
• respiratory weakness with atelectasis
  • systemic lupus erythematosus
  • polymyositis
  • glucocorticoid-induced myopathy
• recurrent respiratory tract infection
• drug-induced interstitial lung disease

More general terms

• pulmonary fibrosis
• chronic lung disease