bronchopulmonary sequestration

Pathology

• a segment of non-functional lung tissue not connected to the bronchial tree
• does not receive itw blood supply from the pulmonary circulation
• can manifest as a large, vascular lower-lobe consolidation
• generally no communication with upper airway
• bacteria may gain access to sequestration through lower pulmonary connections

Clinical manifestations

• recurrent pneumonia

Radiology

• chest CT:
  • an anomalous systemic artery is visible in 2/3 of patients
    • origin most frequently thoracic aorta
    • origin less frequently abdominal aorta or coronay artery
• MRI of thorax may be necessary for diagnosis