craniorachischisis

Epidemiology

• very rare

Pathology

• most severe form of neural tube defect
• both the brain & spinal cord remain open to varying degrees
• craniorachischisis totalis (complete craniorachischisis)
  • anencephaly
  • total spina bifida
  • lethal

Radiology

• fetal ultrasonography for prenatal diagnosis

More general terms

• neural tube defect