arrhythmogenic right ventricular cardiomyopathy type 9; familial arrhythmogenic right ventricular dysplasia type 9 (ARVC9, ARVD9)
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Pathology
- partial degeneration of the myocardium of the right ventricle
- replacement of ventricular myocardium with fatty & fibrous elements
- preferential involvement of the right ventricular free wall
Genetics
- autosomal dominant
- associated with in PKP2
Clinical manifestations
Diagnostic procedures
- electrocardiogram
- coronary angiography
- clinically defined by electrocardiographic & angiographic criteria