keratinocytic non-epidermolytic nevus

Pathology

• benign, pigmented epidermal nevi
• non-epidermolytic

Genetics

• associated with defects in FGFR3

Clinical manifestations

• may vary in their extent from a single (usually linear) lesion to widespread & systematized involvement
• may be present at birth or develop early during childhood

More general terms

• nevus

Database

• OMIM: https://mirror.omim.org/entry/162900