3-methylglutaconic acid

Introduction

3-methylglutaconyl-CoA is intermediate in metabolism of leucine.

Increased amounts found in the urine of patients with methylglutaconyl-CoA hydratase deficiency.

More general terms

• carboxylic acid

Additional terms

• 3-methylglutaconyl-CoA
• methylglutaconyl-CoA hydratase deficiency; methylglutaconic aciduria
• methylglutaconyl-CoA hydratase, mitochondrial; AU-specific RNA-binding enoyl-CoA hydratase; AU-binding protein/enoyl-CoA hydratase (AUH)

Database

• PubChem: http://pubchem.ncbi.nlm.nih.gov/summary/summary.cgi?cid=99884