ATP synthase lipid-binding protein-P3 (mitochondrial ATP synthase, subunit c, isoform 3, ATP5G3)
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Function
- component of mitochondrial membrane ATP synthase FO
Structure
belongs to the ATPase C chain family
Compartment
Pathology
- major protein stored in the storage bodies of animals or humans affected with ceroid lipofuscinosis (Batten disease)
Genetics
- there are 3 genes which encode the mitochondrial ATP synthase proteolipid (ATP5G1) & they specify precursors with different import sequences but identical mature proteins